Case Study

Extrarenal Wilms tumour: A rare cause for retroperitoneal mass in children

Leilah Schoonraad, Anel van Zyl, Bob Banieghbal, Pawel Schubert
South African Journal of Oncology | Vol 10 | a352 | DOI: https://doi.org/10.4102/sajo.v10i0.352 | © 2026 Leilah Schoonraad, Anel van Zyl, Bob Banieghbal, Pawel Schubert | This work is licensed under CC Attribution 4.0
Submitted: 17 September 2025 | Published: 14 July 2026

About the author(s)

Leilah Schoonraad, Department of Paediatric Oncology, Faculty of Paediatrics and Child Health, Stellenbosch University, Cape Town, South Africa
Anel van Zyl, Department of Paediatric Oncology, Faculty of Paediatrics and Child Health, Stellenbosch University, Cape Town, South Africa
Bob Banieghbal, Department of Paediatric Surgery, Faculty of Surgery, Stellenbosch University, Cape Town, South Africa
Pawel Schubert, Department of Anatomical Pathology, Faculty of Anatomical Pathology, Stellenbosch University, Cape Town, South Africa

Abstract

Nephroblastoma (Wilms tumour) is one of the most common paediatric solid tumours, with a prevalence of 5% globally and 13.5% in South Africa. However, extrarenal Wilms tumour (ERWT) is a rare disease, and fewer than 100 cases have been reported in the paediatric age group.
Contribution: In this report, we present the first reported case of extrarenal Wilms tumour, presenting as a retroperitoneal mass to a Paediatric Oncology Unit in South Africa.


Keywords

nephroblastoma; Wilms tumour; extrarenal Wilms tumour; retroperitoneal mass; cytopathology; immunohistochemisty Wilms tumour

Sustainable Development Goal

Goal 3: Good health and well-being

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